Turcot's syndrome: a new case in the first decade of life
β Scribed by E. Scribano; G. Loria; G. Ascenti; E. Cardia; D. Molina; M. Gaeta
- Publisher
- Springer
- Year
- 1995
- Tongue
- English
- Weight
- 663 KB
- Volume
- 20
- Category
- Article
- ISSN
- 0942-8925
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β¦ Synopsis
A case of Turcot's syndrome is described in an 8-yearold girl. Turcot's syndrome is a rare hereditary disease in which malignant glioma of the central nervous system is associated with colonic polyposis. The patient initially presented with a left parietal glioblastoma diagnosed by computed tomography (CT), and was subsequently found to have nonfamilial colonic polyposis.
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