Tumours and hemihypertrophy associated with Wiedemann-Beckwith syndrome
β Scribed by H. -R. Wiedemann
- Publisher
- Springer
- Year
- 1983
- Tongue
- English
- Weight
- 35 KB
- Volume
- 141
- Category
- Article
- ISSN
- 0340-6997
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π SIMILAR VOLUMES
The Beckwith-Wiedemann syndrome (BWS) is an overgrowth malformation syndrome that occurs with an incidence of 1:13,700 births. There is a striking incidence of childhood tumors found in BWS patients. Various lines of investigation have localized "imprinted" genes involved in BWS and associated child
## Background: Children with beckwith-wiedemann syndrome and idiopathic hemihypertrophy (bws/hh) are at increased risk for developing wilms tumor and screening with abdominal sonography is frequently recommended. however, there is a paucity of published data supporting this strategy. the purpose of
The role of screening for early detection of Wilms' tumour (W) in patients with aniridia (A), Beckwith-Weidemann syndrome (BWS) and hemihypertrophy (HH) has been explored. Of the 1,622 Wilms' tumour patients registered with the National Childhood Cancer Registry from 1971 to 1991, 41 were recorded a