Human a-L-fucosidase, purified from placenta, was taken up from the culture medium by skin fibroblasts from patients with fucosidosis (a-L-fucosidase deficiency). The rate of uptake was low (uptake coefficient = 6 x lo-\* ml.mg-l.h-\*). Intracellular a-L-fucosidase activity was directly proportiona
✦ LIBER ✦
Thermostability of human α-l-fucosidase. Relationship to fucosidosis and low-activity serum α-l-fucosidase
✍ Scribed by Jack A. Alhadeff; Grai L. Andrews-Smith
- Book ID
- 113124107
- Publisher
- Elsevier Science
- Year
- 1980
- Weight
- 626 KB
- Volume
- 614
- Category
- Article
- ISSN
- 0005-2744
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