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The fragile X mutation does not have any major effect on the expression of the hypoxanthine phosphoribosyltransferase (HPRT) locus in human fibroblasts

✍ Scribed by Ann-Marie Steen; Suzanne Marcus; Sigrid Sahlén; Karen Brøndum Nielsen; Bo Lambert


Publisher
Springer
Year
1991
Tongue
English
Weight
280 KB
Volume
87
Category
Article
ISSN
0340-6717

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✦ Synopsis


The possible influence of the fragile X mutation at Xq27 on the expression of the neighbouring gene (at Xq26) for hypoxanthine phosphoribosyl transferase (HPRT) was studied by determination of the levels of HPRT-RNA and HPRT enzyme activity in fibroblast cell cultures from 7 fragile X patients. These levels were lower (although not statistically significantly lower) than in normal fibroblast cultures. Hence, these data do not support the notion of a major effect of the fragile X mutation on the expression of the HPRT gene.