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Stüve-Wiedemann dysplasia in a 3 1/2-year-old boy

✍ Scribed by Kozlowski, K.; Tenconi, R.

Publisher
John Wiley and Sons
Year
1996
Tongue
English
Weight
16 KB
Volume
63
Category
Article
ISSN
0148-7299

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✦ Synopsis

Stuve-Wiedemann osteochondrodysplasia is a rare disorder with distinct clinical and diagnostic radiographic findings. The condition is classified as a bent-bone dysplasia with early, lethal outcome. We report on a boy with Stuve-Wiedemann syndrome who is well and alive at the age of 3 '/z years.

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