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Studies on cultured skin fibroblasts from calves with GM1 gangliosidosis

โœ Scribed by B.J. Sheahan; Elizabeth Roche; W.J.C. Donnelly


Book ID
115963290
Publisher
Elsevier Science
Year
1977
Tongue
English
Weight
454 KB
Volume
87
Category
Article
ISSN
0021-9975

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GM1-gangliosidosis: Accumulation of gang
โœ Yoshiyuki Suzuki; Norimasa Nakamura; Kazuko Fukuoka ๐Ÿ“‚ Article ๐Ÿ“… 1978 ๐Ÿ› Springer ๐ŸŒ English โš– 270 KB

Uptake of radioactivity from 14C-galactose into gangliosides by cultured skin fibroblasts was studied. GM3 was the major ganglioside in control human fibroblasts. An increase of GM1 was demonstrated in GM1-gangliosidosis fibroblasts. The degree of GM1 accumulation was correlated with the clinical ty