An ACTH stimulation test was performed in six patients suffering from the cerebro-hepato-renal syndrome of Zellweger. In contrast to controls, no rise in cortisol was observed. None of these patients showed clinical symptoms of adrenal insufficiency. The sudden death, which occurs in this syndrome,
โฆ LIBER โฆ
Striated adrenocortical cells in cerebro-hepato-renal (Zellweger) syndrome
โ Scribed by Goldfischer, Sidney ;Powers, James M. ;Johnson, Anne B. ;Axe, Steven ;Brown, Frank R. ;Moser, Hugo W.
- Publisher
- Springer-Verlag
- Year
- 1983
- Tongue
- English
- Weight
- 532 KB
- Volume
- 401
- Category
- Article
- ISSN
- 0174-7398
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