Steroid-responsive chorea in moyamoya disease
β Scribed by Dr. Steven G. Pavlakis; Steven Schneider; Karen Black; Robert J. Gould
- Publisher
- John Wiley and Sons
- Year
- 1991
- Tongue
- English
- Weight
- 561 KB
- Volume
- 6
- Category
- Article
- ISSN
- 0885-3185
No coin nor oath required. For personal study only.
β¦ Synopsis
We report the case of a 13-year-old boy with disabling chorea due to moyamoya disease. His chorea seemed to improve with steroid therapy. We conclude that steroid therapy may ameliorate moyamoya-associated chorea, and perioperative steroids can confound neurosurgical outcome. We are unable to assess the effect of cerebrovascular bypass procedures on the outcome of chorea in this patient.
π SIMILAR VOLUMES
## Legends to the Video Cerebrotendinous xanthomatosis patient with jaw opening dystonia, which improves with a sensory geste. Bilteral dysmetria, normal extraocular movements, spastic gait, hyperreflexia, and upgoing toes are present. Achilles tendon xanthomas are demonstrated.