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Single aberrant umbilical artery in a fetus with severe caudal defects: Sirenomelia or caudal dysgenesis

✍ Scribed by Perez-Aytes, Antonio; Montero, Luisa; Gomez, Jacinto; Paya, Artemio


Book ID
101216684
Publisher
John Wiley and Sons
Year
1997
Tongue
English
Weight
462 KB
Volume
69
Category
Article
ISSN
0148-7299

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✦ Synopsis


We describe a 1,000-g twin fetus with absent kidneys and ureters, anal atresia and minimal evidence of external genitalia, and hypoplastic lower limbs with absent feet. A postmortem arteriogram showed a large single umbilical artery in direct continuation with the abdominal aorta, a unique anomaly almost always related to sirenomelia. We discuss the possible diagnosis of this case as sirenomelia or caudal dysgenesis, and the controversy as to whether they are two related or separate entities.