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Severe ulcerative panniculitis caused by alpha 1-antitrypsin deficiency: Remission induced and maintained with intravenous alpha 1-antitrypsin

โœ Scribed by Firas Al-Niaimi; Calum Lyon

Book ID
116586525
Publisher
Elsevier Science
Year
2011
Tongue
English
Weight
652 KB
Volume
65
Category
Article
ISSN
1097-6787

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## Abstract Alpha 1 antitrypsin phenotypes and serum levels are presented for a family in which two brothers have Weber Christian disease and ฮฑ1 antitrypsin (PI) Z phenotypes. Clinical histories are described for these two men. A younger brother has the PI Z phenotype but does not have the disease,