Segmental multicystic dysplasia and ureteropelvic junction obstruction in a nonduplicated kidney

✍ Scribed by Adrienne J.K. Carmack; Miguel Castellan; Marcos Perez-Brayfield; Rafael Gosalbez

• Book ID: 116685794
• Publisher: Elsevier Science
• Year: 2006
• Tongue: English
• Weight: 235 KB
• Volume: 41
• Category: Article
• ISSN: 0022-3468
• DOI: 10.1016/j.jpedsurg.2006.01.056

✦ Synopsis

A 2-month-old child presented for evaluation of prenatal hydronephrosis. Imaging studies were consistent with a right duplex system with a dysplastic, nonfunctioning upper pole and lower pole ureteropelvic junction obstruction. We proceeded with removal of the upper pole and pyeloplasty and were surprised to find a single collecting system with a cystic, dysplastic upper pole segment and the absence of an upper pole pelvis or ureter. The rare diagnosis of a segmental multicystic dysplastic kidney with ipsilateral ureteropelvic junction obstruction was made. We present a review of the case and of previous literature on this topic.