✦ LIBER ✦

Scleromyxedema and the dermato-neuro syndrome: case report and review of the literature

✍ Scribed by Kirsten E. Fleming; Divya Virmani; Evelyn Sutton; Richard Langley; Jessica Corbin; Sylvia Pasternak; Noreen M. Walsh

Book ID: 114787653
Publisher: John Wiley and Sons
Year: 2012
Tongue: English
Weight: 762 KB
Volume: 39
Category: Article
ISSN: 0303-6987
DOI: 10.1111/j.1600-0560.2012.01882.x

No coin nor oath required. For personal study only.

✦ Synopsis

Scleromyxedema is a generalized form of lichen myxedematosus which is characterized by a papular and sclerodermoid skin eruption resulting from dermal fibroblast proliferation and mucin deposition. The majority of patients with scleromyxedema have a monoclonal gammopathy, and other systemic manifestations are common. Herein we describe a case of the ‘dermato‐neuro syndrome’, a rare and sometimes fatal neurologic manifestation of scleromyxedema which consists of fever, convulsions and coma, often preceded by a flu‐like prodrome. In addition, we provide a comprehensive summary of previously published cases of the dermato‐neuro syndrome and discuss the current etiopathogenic theories and treatment options for this rare disease.

Fleming KE, Virmani D, Sutton E, Langley R, Corbin J, Pasternak S, Walsh NM. Scleromyxedema and the dermato‐neuro syndrome: case report and review of the literature.

📜 SIMILAR VOLUMES

Scleromyxedema and the dermato-neuro syn

Scleromyxedema and the dermato-neuro syndrome: case report and review of the literature

✍ Kirsten E. Fleming; Divya Virmani; Evelyn Sutton; Richard Langley; Jessica Corbi 📂 Article 📅 2012 🏛 John Wiley and Sons 🌐 English ⚖ 762 KB

Scleromyxedema myopathy: case report and

Scleromyxedema myopathy: case report and review of the literature

✍ David J. Helfrich; E. R. Walker; A. Julio Martinez; Thomas A. Medsger Jr. 📂 Article 📅 1988 🏛 John Wiley and Sons 🌐 English ⚖ 501 KB

Good Response of Scleromyxedema and Derm

Good Response of Scleromyxedema and Dermato-Neuro Syndrome to Treatment With Intravenous Immunoglobulins

✍ I. Bielsa; F. Benvenutti; R.M. Guinovart; C. Ferrándiz 📂 Article 📅 2012 🏛 Elsevier Science 🌐 Spanish ⚖ 741 KB

Fatal scleromyxedema: Report of a case a

Fatal scleromyxedema: Report of a case and review of the literature

✍ Angela Godby; Paul R. Bergstresser; Basem Chaker; Amit G. Pandya 📂 Article 📅 1998 🏛 Elsevier Science 🌐 English ⚖ 113 KB

Sebastian syndrome: Case report and revi

Sebastian syndrome: Case report and review of the literature

✍ Young, Guy; Luban, Naomi L.C.; White, James G. 📂 Article 📅 1999 🏛 John Wiley and Sons 🌐 English ⚖ 195 KB 👁 1 views

Macrothrombocytopenias (MTCP) are a heterogeneous group of disorders associated with thrombocytopenia and giant platelets, and may include other clinical or laboratory findings such as hereditary nephritis, sensorineural deafness, leukocyte inclusions, and cataracts. Patients with MTCP may have mild

Fryns syndrome: Case report and review o

Fryns syndrome: Case report and review of the literature

✍ Gulseren Yucesoy; Yigit Cakiroglu; Eray Caliskan 📂 Article 📅 2008 🏛 John Wiley and Sons 🌐 English ⚖ 155 KB 👁 1 views

## Abstract Fryns syndrome (FS) is a rare malformation. We report a case of FS referred to our clinic at 27 weeks' gestation with a diagnosis of congenital diaphragmatic hernia. Sonographic examination of the fetus revealed a left‐sided diaphragmatic hernia, pulmonary hypoplasia, and a median orofa