✦ LIBER ✦

Resolution of hepatopulmonary syndrome after auxiliary partial orthotopic liver transplantation in abernethy malformation. A case report

✍ Scribed by Sukru Emre; Ronen Arnon; Emil Cohen; Raffaella A. Morotti; Dmitriy Vaysman; Benjamin L. Shneider

Publisher: John Wiley and Sons
Year: 2007
Tongue: English
Weight: 749 KB
Volume: 13
Category: Article
ISSN: 1527-6465
DOI: 10.1002/lt.21349

No coin nor oath required. For personal study only.

✦ Synopsis

Congenital absence of portal vein and extrahepatic portocaval shunt, also referred to as an Abernethy type 1, is a rare malformation of the mesenteric vasculature. A 9-year-old girl presented with dyspnea on exertion and orthodeoxia. A diagnosis of an Abernethy malformation type 1b and hepatopulmonary syndrome (HPS) was made, and she underwent auxiliary partial orthotopic liver transplantation (APOLT). Symptoms and signs of HPS resolved 2 months after the operation. HPS in Abernethy syndrome is a manifestation of normal portal blood flow bypassing the liver and can be ameliorated by redirecting blood flow to a segment of liver with normal portal anatomy. APOLT is a feasible and successful surgical procedure for patients with Abernethy malformation and HPS.

📜 SIMILAR VOLUMES

Nitric oxide treatment of severe hypoxem

Nitric oxide treatment of severe hypoxemia after liver transplantation in hepatopulmonary syndrome: Case report

✍ Alexander, J ;Greenough, A ;Baker, A ;Rela, M ;Heaton, N ;Potter, D 📂 Article 📅 1997 🏛 Wiley (John Wiley & Sons) 🌐 English ⚖ 73 KB

Pulmonary hypertension after liver trans

Pulmonary hypertension after liver transplantation in patients with antecedent hepatopulmonary syndrome: A report of 2 cases and review of the literature

✍ Federico Aucejo; Charles Miller; David Vogt; Bijan Eghtesad; Shunichi Nakagawa; 📂 Article 📅 2006 🏛 John Wiley and Sons 🌐 English ⚖ 79 KB 👁 1 views

Hepatopulmonary syndrome (HPS) and portopulmonary hypertension (PPHTN) are distinct clinical entities that may complicate liver disease. Although HPS and PPHTN are different, several reports describe 6 patients in whom both conditions have occurred, either concurrently or sequentially, sometimes wit