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Recombinant GM2-Activator Protein Stimulates In Vivo Degradation of GA2 in GM2 Gangliosidosis AB Variant Fibroblasts But Exhibits No Detectable Binding of GA2 in an In Vitro Assay

✍ Scribed by Uwe Bierfreund; Thorsten Lemm; Alexander Hoffmann; Gunther Uhlhorn-Dierks; Robert A. Childs; Chun-Ting Yuen; Ten Feizi; Konrad Sandhoff


Book ID
110421278
Publisher
Springer
Year
1999
Tongue
English
Weight
865 KB
Volume
24
Category
Article
ISSN
0364-3190

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