Neutrophil elastase in patients with hom
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Samarkos, M.; Aessopos, A.; Fragodimitri, C.; Karagiorga, M.; Kalotychou, V.; Vo
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Article
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2000
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John Wiley and Sons
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English
β 44 KB
In this study we investigated the possible role of neutrophil (PMN) elastase and its natural inhibitor, β£1-proteinase inhibitor (β£1-PI) in the pathogenesis of the pseudoxanthoma elasticum (PXE)-like syndrome which is found in patients with homozygous β€-thalassemia. We studied 30 β€-thalassemia homozy