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Proteus syndrome: Course of a severe case

✍ Scribed by Malamitsi-Puchner, Ariadne ;Dimitriadis, Dimitris ;Bartsocas, Christos ;Wiedemann, H.-R.

Publisher: John Wiley and Sons
Year: 1990
Tongue: English
Weight: 304 KB
Volume: 35
Category: Article
ISSN: 0148-7299
DOI: 10.1002/ajmg.1320350228

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✦ Synopsis

We report on the course of a 4l/z-year-old boy with Proteus syndrome who was first described 3 years ago. Details are given on the phenotypic changes, the complications of corrective surgery on tissue overgrowth, and the development of a mesothelioma of the tunica vaginalis of the testis.

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