Accumulation of pristanic acid (2, 6, 10
โ
A. Poulos; P. Sharp; A. J. Fellenberg; D. W. Johnson
๐
Article
๐
1988
๐
Springer
๐
English
โ 485 KB
The plasma of some patients with biochemical evidence of a generalised peroxisomal dysfunction (GPD) show greatly increased levels of phytanic acid as well as its a-oxidation product, pristanic acid (2, 6, 10, 14-tetramethylpentadecanoic acid). Increased amounts of 14-and 16-carbon branched chain fa