✦ LIBER ✦

Primary biliary cirrhosis and the crest syndrome: New terminology?

✍ Scribed by Owen Epstein

Publisher: John Wiley and Sons
Year: 1988
Tongue: English
Weight: 145 KB
Volume: 8
Category: Article
ISSN: 0270-9139
DOI: 10.1002/hep.1840080137

No coin nor oath required. For personal study only.

✦ Synopsis

The syndrome of primary biliary cirrhosis and limited scleroderma (the CREST syndrome) is described in 22 patients. The syndrome is expanded to include a serologic marker-the anticentromere antibody-and keratoconjunctivitis sicca. The acronym "PACK" (primary biliary cirrhosis, anticentromere antibody, CREST syndrome, and keratoconjunctivitis sicca) with "syndrome" is suggested to facilitate recall of the various components of this entity.

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