Beare-Stevenson cutis gyrata syndrome
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Hall, Bryan D. ;Cadle, Ronald G. ;Golabi, Mahin ;Morris, Colleen A. ;Cohen, M. M
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Article
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1992
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John Wiley and Sons
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English
⚖ 813 KB
Beare-Stevenson cutis gyrata syndrome consists of skin furrows of corrugated appearance, acanthosis nigricans, craniofacial anomalies, particularly craniosynostosis a n d ear defects, anogenital anomalies, skin tags, and prominent umbilical stump. Four cases of this striking syndrome are reported. T