𝔖 Bobbio Scriptorium
✦   LIBER   ✦

Preemptive Living Donor Liver Transplantation in Glycogen Storage Disease Ia: Case Report

✍ Scribed by S. Kaihara; H. Ushigome; K. Sakai; A. Yoshizawa; S. Nobori; T. Suzuki; M. Okamoto; T. Ochiai; N. Yoshimura

Book ID
116934525
Publisher
Elsevier Science
Year
2008
Tongue
English
Weight
200 KB
Volume
40
Category
Article
ISSN
0041-1345

No coin nor oath required. For personal study only.

πŸ“œ SIMILAR VOLUMES

Living donor liver transplantation for g
Living donor liver transplantation for glycogen storage disease type Ib
✍ Mureo Kasahara; Reiko Horikawa; Seisuke Sakamoto; Takanobu Shigeta; Hideaki Tana πŸ“‚ Article πŸ“… 2009 πŸ› John Wiley and Sons 🌐 English βš– 80 KB

Glycogen storage disease type 1b (GSD-1b) is due to an autosomal recessive inborn error of carbohydrate metabolism caused by defects in glucose-6-phosphatase translocase. Patients with GSD-1b have severe hypoglycemia with several clinical manifestations of hepatomegaly, obesity, a doll-like face, an

Combined liver-kidney transplantation in
Combined liver-kidney transplantation in glycogen storage disease Ia: A case beyond the guidelines
✍ Mirco Belingheri; Luciana Ghio; Ambra Sala; Francesca Menni; Laura Trespidi; Mar πŸ“‚ Article πŸ“… 2007 πŸ› John Wiley and Sons 🌐 English βš– 67 KB

Glycogen storage disease type Ia (GSD Ia) is a rare metabolic disorder due to hepatic glucose-6-phosphatase deficiency. Although great progress has been made in managing affected patients, severe hypoglycemia, lactic acidosis, hyperlipidemia, hepatic cytolysis, and impaired kidney function are frequ