✦ LIBER ✦

Poster Session I Abstracts

Publisher: Wiley (John Wiley & Sons)
Year: 2009
Tongue: English
Weight: 676 KB
Volume: 92
Category: Article
ISSN: 0006-3525
DOI: 10.1002/bip.21224

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📜 SIMILAR VOLUMES

Poster Session Abstracts: Abstracts 1–68

📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 292 KB

The vast majority of cases of cystic Þbrosis are the result of a single amino acid deletion (DF508) in the sequence of CFTR. The result of this deletion is that the DF-CFTR misfolds and does not obtain its normal residence in the plasma membrane of cells, but instead is proteolyzed. The F508-contain

Poster Session Abstracts: Abstracts 69–1

Poster Session Abstracts: Abstracts 69–148

📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 369 KB

## Cystic Fibrosis Conference which occurs in the intermediate and Golgi compartments. This may reßect either a somewhat different route through the secretory pathway or interference with the enzymatic steps in oligosaccharide processing possibly by calnexin. The latter possibility is being explore

Poster Session Abstracts: Abstracts 149–

Poster Session Abstracts: Abstracts 149–215

📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 335 KB

The nasal potential difference (PD) technique allows measurement of airway ion transport in human subjects in vivo. The characteristic abnormalities found in CF, namely increased Na + absorption and decreased cAMP-regulated Cl -secretion can be measured by sequential perfusion with amiloride, low Cl

Poster Session Abstracts: Abstracts 216–

Poster Session Abstracts: Abstracts 216–281

📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 324 KB

tgAAVCF (AAV-CFTR) was used in a phase II, double-blind, randomized, placebo-controlled clinical trial to transfer CFTR cDNA into respiratory epithelial cells in the maxillary sinus of 23 CF patients with maxillary antrostomies. The maxillary sinuses serve as a surrogate model of CF lung disease bec

Poster Session Abstracts: Abstracts 282–

Poster Session Abstracts: Abstracts 282–341

📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 277 KB

The disturbances in ionic conductances and water transport associated with mutations in CFTR ultimately result in impairments in mucociliary clearance (MCC). The resulting mucostasis provides a conducive environment for colonization by opportunistic microorganisms that can induce severe inßammatory

Poster Session Abstracts: Abstracts 342–

Poster Session Abstracts: Abstracts 342–425

📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 358 KB

We describe the clinical features of 20 patients from Sicily who have rare genotypes. For each patient, the age of diagnosis, the present age, the sweat test value for chloride, meconium ileus, diabetes, nasal polyps, age of lung colonisation by Pseudomonas aeruginosa and liver involvement are recor