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PO8.4 Clinical Improvement with Pyridostigmine in Limb-Girdle Myasthenia with Tubular Aggregates

✍ Scribed by Dae-Seong Kim; Hee Young Jo


Book ID
119607750
Publisher
Elsevier Science
Year
2009
Tongue
English
Weight
60 KB
Volume
120
Category
Article
ISSN
1388-2457

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Familial limb-girdle myasthenia with tub
✍ Eisuke Furui; Koji Fukushima; Toshio Sakashita; Shunichi Sakato; Shiro Matsubara πŸ“‚ Article πŸ“… 1997 πŸ› John Wiley and Sons 🌐 English βš– 242 KB

Two sisters developed slowly progressive limb-girdle weakness in their childhood. The weakness responded to acetylcholinesterase inhibitors. Repetitive nerve stimulation showed decremental responses and single-fiber electromyography demonstrated increased jitter and blocking. Needle electromyography