𝔖 Bobbio Scriptorium
✦   LIBER   ✦

Persisting “Writer's Cramp” as a result of compensation of a temporary palsy due to a hereditary neuropathy with liability to pressure palsies

✍ Scribed by Dr. Andreas Straube; Norbert Mai; Ernst Walther; Michael Mayer

Publisher
John Wiley and Sons
Year
1996
Tongue
English
Weight
383 KB
Volume
11
Category
Article
ISSN
0885-3185

No coin nor oath required. For personal study only.

✦ Synopsis

Abstract

A 49‐year‐old man reported several periods of acute paresis of different nerves after exposure to pressure. All palsies showed a good recovery over a period of days to months. The suspected diagnosis of a hereditary neuropathy with liability to pressure palsies was confirmed by the histology of a suralis nerve biopsy, which showed a distinct tomaculous swelling of the myelin. Nine years ago he noticed an acute, distally pronounced palsy of the right arm. A brachial plexus lesion was diagnosed. His profession required written work, thereby forcing him to compensate this weakness by increasign the coactivation of the elbow and upper arm. This coactivation persisted even after complete recovery from the plexus palsy. Thus, the patient showed the typical feature of classcal writer's cramp, with broad coactivation of the arm muscles, which has continued to the present. At the same time, however, the patient was able to perform other motoric tasks well, such as painting. After several practice sessions with a special program that makes use of preserved motor abilities to reestablish writing, the patient was again able to write with a normal kinematic profile as documented by the recorded handwriting. This suggests that the “writer's cramp” of our patient is one form of task‐related dystonia that may be related more to the perserveration of a misleading motor strategy than to a general inability of the motor system to control the movement properly.

📜 SIMILAR VOLUMES

Fulminant case of hereditary neuropathy
Fulminant case of hereditary neuropathy with liability to pressure palsy
✍ Brian A. Crum; Eric J. Sorenson; Gregorio A. Abad; P. James B. Dyck 📂 Article 📅 2000 🏛 John Wiley and Sons 🌐 English ⚖ 139 KB

Hereditary neuropathy with liability to pressure palsy (HNPP) is typified as isolated nerve palsies caused by trivial compression or trauma. It rarely presents in two extremities and even more infrequently affects all four limbs simultaneously. We present a patient who concurrently experienced right

Recurrent brachial plexus palsies as the
Recurrent brachial plexus palsies as the only clinical expression of hereditary neuropathy with liability to pressure palsies associated with a de novo deletion of the peripheral myelin protein-22 gene
✍ Florian Stögbauer; Peter Young; Max Kerschensteiner; E. Bernd Ringelstein; Gerd 📂 Article 📅 1998 🏛 John Wiley and Sons 🌐 English ⚖ 72 KB 👁 2 views

There is phenotypic heterogeneity in patients with hereditary neuropathy with liability to pressure palsies. In rare cases, recurrent brachial plexopathy is the only expression of the disease. We describe a patient with three episodes of plexus brachialis palsy and a de novo deletion of the peripher