𝔖 Bobbio Scriptorium
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PELIZAEUS-MERZBACHER DISEASE: BRAIN LIPID AND FATTY ACID COMPOSITION

✍ Scribed by J. M. Bourre; J. H. Bornhofen; C. A. Araoz; O. Daudu; N. A. Baumann

Book ID
111170277
Publisher
John Wiley and Sons
Year
1978
Tongue
English
Weight
494 KB
Volume
30
Category
Article
ISSN
0022-3042

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## Abstract Duplication of __PLP1__, an X‐linked gene encoding the major myelin membrane protein of the human CNS, is the most frequent cause of Pelizaeus‐Merzbacher disease (PMD). Transgenic mice with extra copies of the wild type __Plp1__ gene, a valid model of PMD, also develop a dysmyelinating