Three members of a family in one generation were affected by a pattern dystrophy of the retinal pigment epithelium. The patients present typical hyperpigmented macular RPE lesions in a butterfly-shaped to (macro-)reticular pattern, and were all asymptomatic. Examination of 26 family members in 3 gen
Pattern dystrophy of the retinal pigment epithelium
β Scribed by K. U. Duinkerke-Eerola; A. Pinckers; J. R. M. Cruysberg
- Publisher
- Springer Netherlands
- Year
- 1987
- Tongue
- English
- Weight
- 575 KB
- Volume
- 11
- Category
- Article
- ISSN
- 0165-5701
No coin nor oath required. For personal study only.
π SIMILAR VOLUMES
There is no ideal electrophysiological test for retinal pigment epithelial (RPE) function. The light-induced responses (EOG, c-wave, fast oscillation) that require photoreception are not pure RPE signals, and even the widely-used EOG has not been associated with any specific physiological disturbanc
At present it is difficult to distinguish those human chorioretinal diseases in which the retinal pigment epithelium (RPE) is the primary site of dysfunction. This difficulty is caused by several factors such as scarcity of biochemical and histological information and a lack of correlation of basic
The retinal pigment epithelium (RPE) is essential for retinoid recycling and phagocytosis of photoreceptors. Understanding of proteome changes that mediate oxidative stress-induced degeneration of RPE cells may provide further insight into the molecular mechanisms of retinal diseases. In the current