## Background: Children with beckwith-wiedemann syndrome and idiopathic hemihypertrophy (bws/hh) are at increased risk for developing wilms tumor and screening with abdominal sonography is frequently recommended. however, there is a paucity of published data supporting this strategy. the purpose of
Partial nephrectomy for Wilms' tumor in a child with hemihypertrophy
β Scribed by Raney, R. Beverly ;D'Angio, Giulio J. ;Bishop, Harry C. ;Betts, James ;Chatten, Jane
- Publisher
- John Wiley and Sons
- Year
- 1985
- Tongue
- English
- Weight
- 315 KB
- Volume
- 13
- Category
- Article
- ISSN
- 0098-1532
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β¦ Synopsis
This 3-year-old white female has been followed by members of the Division of General Surgery since the age of 3 months. She was referred to the Children's Hospital of Philadelphia at that time because of bilateral inguinal hernias. Physical examination showed hemihypertrophy, with the right leg being larger than the left. An intravenous urogram was normal. The left kidney was 7.2 cm in length; the right kidney was 6.8 cm long. Since that time she has undergone periodic ultrasonographic examinations of the kidneys, because of the wellknown association between the presence of hemihypertrophy and the increased risk of eventual intraabdominal malignancy. In October, 1982, an ultrasonogram showed for the first time a mass in the upper pole of the left kidney. She was admitted in order that further studies might be carried out, with the thought that partial nephrectomy might be feasible.
π SIMILAR VOLUMES
## Abstract To evaluate the usefulness of regular radiographic screening to detect an asymptomatic intraabdominal tumor in patients with an increased risk of developing Wilms tumor, we reviewed the files of patients with hemihypertrophy, aniridia, or BeckwithβWiedemann syndrome who were registered