Various mutations of genes encoding type I procollagen chains have been linked to osteogenesis imperfecta (OI). The mutations yield abnormal procollagen molecules that fold improperly. HSP 47, a stress-inducible protein localized to the endoplasmic reticulum (ER) of collagen-producing cells, may par
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[Part 2: Biological Sciences] || Thermal Stability of Type I and Type III Procollagens from Normal Human Fibroblasts and from a Patient with Osteogenesis Imperfecta
β Scribed by Leena Peltonen, Aarno Palotie, Toshihiko Hayashi and Darwin J. Prockop
- Book ID
- 123663401
- Publisher
- National Academy of Sciences
- Year
- 1980
- Tongue
- English
- Weight
- 1023 KB
- Volume
- 77
- Category
- Article
- ISSN
- 0027-8424
- DOI
- 10.2307/8162
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