P0165 CO-EXISTENCE OF GOUGEROT SJÖGREN SYNDROME AND BEHÇET DISEASE: REPORT OF THREE CASES

Jeune syndrome and liver disease: Report

Jeune syndrome and liver disease: Report of three cases treated with ursodeoxycholic acid

✍ Labrune, Philippe; Fabre, Monique; Trioche, Pascale; Estournet-Mathiaud, Brigitt 📂 Article 📅 1999 🏛 John Wiley and Sons 🌐 English ⚖ 33 KB 👁 2 views

Three children with Jeune syndrome (asphyxiating thoracic dystrophy) had clinical and laboratory evidence of liver disease. In two patients the disease evolved to biliary cirrhosis, whereas in the third it was recognized when extensive fibrosis was developing. In the three patients, treatment with u