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Normal plasma somatomedin activity in hydrocortisone-treated congenital adrenal hyperplasia

✍ Scribed by R. Rappaport; C. Prevot


Book ID
119455903
Publisher
Elsevier Science
Year
1977
Tongue
English
Weight
185 KB
Volume
90
Category
Article
ISSN
1097-6833

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Classical congenital adrenal hyperplasia (CAH) results from an inherited enzymatic defect in cortisol synthesis and more than 90 per cent of cases are due to 21-hydroxylase deficiency. The androgen excess associated with this condition typically results in ambiguous external genitalia in affected fe