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Neuronal intranuclear inclusion disease in two adult siblings

✍ Scribed by Thomas D. Bird; S. Mark Sumi; Michael D. Schuffler


Publisher
John Wiley and Sons
Year
1985
Tongue
English
Weight
232 KB
Volume
17
Category
Article
ISSN
0364-5134

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## Abstract Neuronal intranuclear inclusion disease (NIID) is a rare neurodegenerative disorder with a heterogeneous clinical picture characterized by the presence of eosinophilic intranuclear inclusions in neuronal and glial cells. We describe a case, reported 12 years ago as dopa‐responsive dysto