✦ LIBER ✦

Neurofibromatosis of the head and neck

✍ Scribed by Maceri, Dennis R. ;Saxon, Keith G.

Publisher: Wiley (John Wiley & Sons)
Year: 1984
Weight: 771 KB
Volume: 6
Category: Article
ISSN: 0148-6403
DOI: 10.1002/hed.2890060407

No coin nor oath required. For personal study only.

✦ Synopsis

Neurofibromatosis (von Recklinghausen's disease) is an autosomal dominant disease that affects one in 2,500-3,000 births. Because the head and neck is unique in its anatomical compartmentalization of the central and peripheral nervous systems, the potential for involvement of these areas with neurofibromas is substantial and accounts for a myriad of clinicopathologic presentations. In the present study, the incidence of involvement in the head and neck is 37%. We found 81% of the patients had cafe au lait spots, 63% had positive family histories, and 66% had multiple cutaneous nodules. An incidence of malignant transformation was documented in 3.5% of the cases. Management of benign neurofibromatosis must be individualized for each patient and ranges from incisional biopsy to wide local excision. In every case, the risk of severe neurologic deficit must be weighed against the benefits of surgical resection, which is usually incomplete. Genetic counseling is advised for all patients with this disease, since no cure is available.

📜 SIMILAR VOLUMES

Head and Neck Sarcoma: Report of the Hea

Head and Neck Sarcoma: Report of the Head and Neck Sarcoma Registry

✍ Drs Harold J. Wanebo; Drs R. James Koness; Dr. John K. Macfarlane; Dr. Frederick 📂 Article 📅 1992 🏛 John Wiley and Sons 🌐 English ⚖ 581 KB

A Head and Neck Sarcoma Registry was established by the Society of Head and Neck Surgeons to review treatment results of a rare tumor by surgeons with special interest in this anatomic site. Two hundred fourteen patients were analyzed. There were 194 adult tumors and 20 pediatric tumors. The major s

Cytopathology of the Head and Neck

✍ Ricardo H. Bardales 📂 Article 📅 1999 🏛 John Wiley and Sons 🌐 English ⚖ 22 KB 👁 2 views

Pilomatrixoma of the head and neck

✍ Toback, Jeffrey M. ;Hoover, Larry A. ;Dudley, James P. 📂 Article 📅 1984 🏛 Wiley (John Wiley & Sons) ⚖ 432 KB 👁 1 views

Pilomatrixoma is an uncommon neoplasm which occurs most frequently in the head and neck region. It usually presents as a slowly growing dermal or subcutaneous mass. Unfamiliarity with this lesion may lead the physician to mistake it for more common infectious or neoplastic processes. Most pilomatrix

Fibroxanthosarcoma of the head and neck

✍ Harry A. McColl JR.; Gene H. Moore 📂 Article 📅 1979 🏛 John Wiley and Sons 🌐 English ⚖ 634 KB

## Fibroxanthosarcoma of the Head and Neck .

Morbidity of the neck after head and nec

Morbidity of the neck after head and neck cancer therapy

✍ C. Paul van Wilgen; Pieter U. Dijkstra; Berend F. A. M. van der Laan; John T. Pl 📂 Article 📅 2004 🏛 John Wiley and Sons 🌐 English ⚖ 91 KB 👁 2 views

## Abstract ## Background. Studies on morbidity of the neck after head and neck cancer therapy are scarcely described. ## Methods. Patients who underwent surgery, including neck dissection, with and without radiation therapy at least 1 year before the study were asked to participate. We assessed

Embryonal rhabdomyosarcoma of the head a

Embryonal rhabdomyosarcoma of the head and neck

✍ Oliver Moore; Carlo Grossi 📂 Article 📅 1959 🏛 John Wiley and Sons 🌐 English ⚖ 458 KB 👁 2 views