## Abstract BeckwithโWiedemann syndrome (BWS) is an overgrowth syndrome associated with macroglossia, abdominal wall defects, ear anomalies, and an increased risk for embryonic tumors. Reported tumor risk estimates vary between 4% and 21%. It has been hypothesized that tumor predisposition in BWS i
Nephromegaly in infancy and early childhood: A risk factor for Wilms tumor in Beckwith-Wiedemann syndrome
โ Scribed by Michael R. DeBaun; Marilyn J. Siegel; Peter L. Choyke
- Book ID
- 117165944
- Publisher
- Elsevier Science
- Year
- 1998
- Tongue
- English
- Weight
- 136 KB
- Volume
- 132
- Category
- Article
- ISSN
- 1097-6833
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## Background: Children with beckwith-wiedemann syndrome and idiopathic hemihypertrophy (bws/hh) are at increased risk for developing wilms tumor and screening with abdominal sonography is frequently recommended. however, there is a paucity of published data supporting this strategy. the purpose of
## Background: We undertook a cost-benefit analysis of screening for wilms tumor and hepatoblastoma in children with beckwith-wiedemann syndrome (bws), a known cancer predisposition syndrome. the purpose of this analysis was twofold: first, to assess whether screening in children with bws has the p
## Abstract To evaluate the usefulness of regular radiographic screening to detect an asymptomatic intraabdominal tumor in patients with an increased risk of developing Wilms tumor, we reviewed the files of patients with hemihypertrophy, aniridia, or BeckwithโWiedemann syndrome who were registered