## Abstract Duplication of __PLP1__, an X‐linked gene encoding the major myelin membrane protein of the human CNS, is the most frequent cause of Pelizaeus‐Merzbacher disease (PMD). Transgenic mice with extra copies of the wild type __Plp1__ gene, a valid model of PMD, also develop a dysmyelinating
Myelination of a fetus with Pelizaeus–Merzbacher disease: Immunopathological study
✍ Scribed by Kazuhiro Shiraishi; Masayuki Itoh; Kenji Sano; Sachio Takashima; Takeo Kubota
- Publisher
- John Wiley and Sons
- Year
- 2003
- Tongue
- English
- Weight
- 168 KB
- Volume
- 54
- Category
- Article
- ISSN
- 0364-5134
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