Nine patients with adult-onset acid maltase deficiency (Pompe's disease) were examined clinically and with computed tomography (CT). The CT scan showed early and severe involvement of the muscles of trunk and thighs, with selective sparing of the tensor fasciae latae, short head of biceps femoris, g
Muscle MRI in adult-onset acid maltase deficiency
β Scribed by Anna Pichiecchio; Carla Uggetti; Sabrina Ravaglia; Maria Grazia Egitto; Miriam Rossi; Giorgio Sandrini; Cesare Danesino
- Book ID
- 116792126
- Publisher
- Elsevier Science
- Year
- 2004
- Tongue
- English
- Weight
- 113 KB
- Volume
- 14
- Category
- Article
- ISSN
- 0960-8966
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