Multiple trichoepithelioma occluding both external auditory canals

✍ Scribed by Dr. Carmel O. Bibi; Drs. Dan M. Fliss; Ilana Avinoach; Hillel Brenner; Ferrit Tovi

• Book ID: 102237502
• Publisher: John Wiley and Sons
• Year: 1990
• Tongue: English
• Weight: 422 KB
• Volume: 12
• Category: Article
• ISSN: 1043-3074
• DOI: 10.1002/hed.2880120312

✦ Synopsis

Multiple trichoepithelioma is an uncommon skin disease with autosomal dominant transmission. It is characterized by multiple, benign facial skin lesions. These lesions constitute a formidable cosmetic and therapeutic problem. Treatment modalities are numerous and varied. In a few rare cases, confluence of the lesions may result in occlusion of the auditory canal, with consequent loss of hearing. In such cases the treatment of choice should be excision and split-thickness skin grafting. HEAD & NECK 12~257-260,1990

Multiple trichoepithelioma, which has many synonyms, was first described by Brooke' and Fordyce.2 They used the terms epithelioma adenoides cysticum and multiple benign cystic epithelioma in 1892. Jarisch3 later coined the term trichoepithelioma papulosum multiplex, indicating that the multiple papules originated in the hair follicles.

Multiple trichoepithelioma is an uncommon, benign, cutaneous neoplasm with an autosomal dominant pattern of inheritance. A similar le-From the Departments of Plastic Surgery (Dr. Bibi). Ear, Nose and Throat (Drs. Fliss, Brenner, and Tovi), and Pathology (Avinoach).