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Moving toes and myoclonus associated with hereditary neuropathy with liability to pressure palsy (HNPP)

โœ Scribed by Aziz Shaibani; Clifton Gooch; Yadollah Harati

Publisher
John Wiley and Sons
Year
1997
Tongue
English
Weight
181 KB
Volume
20
Category
Article
ISSN
0148-639X

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โœฆ Synopsis

A 22-year-old male awoke with right foot drop and numbness.

CASE OF THE MONTH

Nerve conduction studies, sural nerve biopsy, and molecular genetic analysis were consistent with hereditary neuropathy with liability to pressure palsy Section Editors (HNPP). Two months later he developed involuntary flexion/extension movements of the right toes with associated intermittent dystonic flexion of the Robert C. Griggs, MD right foot. Over the next 2 months these movements spread to the left foot Rochester, New York and hand and myoclonus of the left trapezius and rhomboid appeared. This Jerry R. Mendell, MD is the first case report of moving toes syndrome and segmental myoclonus Columbus, Ohio in association with HNPP. The temporal and topographic patterns of spread of the abnormal movements suggest a central mechanism probably induced

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