The uptake and catabolism of [3H-ceramide]-GM1 was followed in living fibroblasts from patient with different forms of beta-galactosidase deficiency. Gangliosides are identified according to the nomenclature of Svennerholm (1963). A total inability to metabolize the ingested substrate was found in i
โฆ LIBER โฆ
Metabolic activities in human skin fibroblasts preloaded with labeled GM2-ganglioside
โ Scribed by Srinivasa Raghavan; Timothy A. Lyerla; Allan Krusell; Edwin H. Kolodny
- Book ID
- 115739848
- Publisher
- Elsevier Science
- Year
- 1987
- Tongue
- English
- Weight
- 704 KB
- Volume
- 917
- Category
- Article
- ISSN
- 0005-2760
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