Cognitive dissection of Williams Syndrom
β Wang, Paul P.
π Article
π
1999
π John Wiley and Sons
π English
β 3 KB
π 1 views
β¦ LIBER β¦
Longitudinal study of the cognitive development in children with Williams-Beuren syndrome
β Scribed by Gosch, Angela ;Pankau, Rainer
- Publisher
- John Wiley and Sons
- Year
- 1996
- Tongue
- English
- Weight
- 18 KB
- Volume
- 61
- Category
- Article
- ISSN
- 0148-7299
- DOI
- 10.1002/(sici)1096-8628(19960102)61:1<26::aid-ajmg5>3.0.co;2-v
No coin nor oath required. For personal study only.
β¦ Synopsis
Clin Res 38:536Al reported stability of IQs in a group of 14 children with Williams-Beuren syndrome (WBS) over a 5-year period and concluded that they display a development rate similar to normal children. The aim of our study was to examine the stability of the development of nonverbal reasoning abilities over a period of 2 years using two methods. We studied 18 children with WBS (9 girls, 9 boys) with a mean age of 6.6 years (range: 4.4-10.6 yr) at year one (Tl), and approximately two years later (T2) at the average age of 8.6 years (range: 5.11-12.7 yr). The Columbia Mental Maturity Scale (CMM) and the Draw A Person Test were administered. The results show that the IQs resulting from the Draw A Person Test were stable over the 2-year period (Tl: mean I& = 63.5, T2: mean IQ = 65, t = 0.63), and display a significant correlation between the two methods (r = 0.547, P = 0.01). Furthermore, the correlation between the two tests (CMM and Draw A Person Test) at the second assessment is high and significant (r = 0.56, P = 0.01). The mean IQs at T2 can be classified as mild mental retardation. A notable result is the significant decrease of the IQs according to the CMM (Tl: mean IQ = 77, T2: mean I& = 68, t = 2.69, P = 0.01). These results suggest that the developmental outcome of children with WBS varies in specific areas of cognitive function over a 2-year period.
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