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Living-related liver transplantation for neonatal-onset propionic acidemia

โœ Scribed by Tohru Yorifuji; Junko Muroi; Ayumi Uematsu; Tatsutoshi Nakahata; Hiroto Egawa; Koichi Tanaka


Book ID
117847465
Publisher
Elsevier Science
Year
2000
Tongue
English
Weight
52 KB
Volume
137
Category
Article
ISSN
1097-6833

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Liver transplantation for propionic acid
โœ Roshni Vara; Charles Turner; Helen Mundy; Nigel D. Heaton; Mohammed Rela; Giorgi ๐Ÿ“‚ Article ๐Ÿ“… 2011 ๐Ÿ› John Wiley and Sons ๐ŸŒ English โš– 146 KB ๐Ÿ‘ 1 views

Propionic acidemia (PA) is a rare inherited disorder of branched chain amino acid metabolism; despite improvements in conventional medical management, the long-term outcome remains disappointing. Liver transplantation (LT) has been proposed to minimize the risk of further metabolic decompensations a