Liver transplantation with reconstruction of infrarenal vena cava and iliac veins

✍ Scribed by Ruud A.F. Krom

• Book ID: 102467690
• Publisher: John Wiley and Sons
• Year: 2004
• Tongue: English
• Weight: 153 KB
• Volume: 10
• Category: Article
• ISSN: 1527-6465
• DOI: 10.1002/lt.20197

✦ Synopsis

A 31-year-old lawyer presented with bouts of severe encephalopathy. He was diagnosed with a1-antitrypsin deficiency type MZ. In addition, his mobility was poor due to markedly edematous legs. At birth, he underwent exchange transfusion for rhesus (Rh)-antagonism, which caused umbilical vein sepsis and subsequent portal vein thrombosis. He underwent a splenorenal shunt operation for repeated variceal bleeds, which soon failed due to thrombosis of the shunt. The upper gastrointestinal bleeds were treated conservatively until the age of 9 years, when he received a Marion-Clatworthy shunt 1,2 (Fig. 1). While he no longer experienced upper gastrointestinal bleeds, he progressively suffered from swelling of both legs and encephalopathy, which interfered significantly with mobility and his profession as a lawyer.