Liver transplantation (LT) is the only curative option for patients with familial amyloid polyneuropathy (FAP) at present. Twenty patients with FAP underwent LT between May 1998 and June 2007. Transthyretin mutations included predominantly the Val30Met mutation but also 10 other mutations. Seven pat
Liver transplantation in familial amyloidotic polyneuropathy (FAP). A comparative study of transplanted and non-transplanted patient's survival
✍ Scribed by O. B. Suhr; Y. Ando; G. Holmgren; L. Wikström; S. Friman; G. Herlenius; B.-G. Ericzon
- Publisher
- Springer
- Year
- 1998
- Tongue
- English
- Weight
- 177 KB
- Volume
- 11
- Category
- Article
- ISSN
- 0934-0874
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📜 SIMILAR VOLUMES
Familial amyloidotic polyneuropathy is an inherited form of amyloidosis associated with a mutant form of a protein called transthyretin. The Methionine-30 variant is the most frequent mutation observed. This disorder is caused by deposition of this protein as amyloid in several organs, such as the h
Cumulative recurrence after surgical resection for hepatocellular carcinoma (HCC) is very high. Several retrospective analyses have shown that liver transplantation was more effective than resection for patients with HCC at early tumor stages. Consequently, in January 1990, we decided to prospective
The efficacy of tranexamic acid (TA) and aprotinin (AP) in reducing blood product requirements in orthotopic liver transplantation (OLT) was compared in a prospective, randomized and double-blind study. One hundred and twenty seven consecutive patients undergoing OLT were enrolled; TA was administer
The cause and timing of first liver allograft failure was evaluated in 177 patients who underwent a second liver transplant between January 1984 and December 1988. The population studied consisted of 94 men and 83 women with a mean age 41.3 +/- 1.0 yr (mean +/- S.E.M.). Mean first-graft survival was
lung Klinische Chemie II; 2 Zentrum Innere Medizin und Dermatologie, Abteilung fu ¨r Gastroenterologie und Hepatologie; 3 Zentrum Chirurgie, Abteilung Abdominal-und Trans-ing period and final outcome of these patients. Protein calorie plantations-Chirurgie, Konstanty-Gutschow-Straße 8, 30625 Hannove