✦ LIBER ✦

Liver transplantation for cardiac failure in patients with hereditary hemorrhagic telangiectasia

✍ Scribed by Thierry Thevenot; Claire Vanlemmens; Vincent Di Martino; Marie-Claude Becker; Pierre-Olivier Denue; Bernadette Kantelip; Solange Bresson-Hadni; Bruno Heyd; Georges Mantion; Jean-Philippe Miguet

Publisher: John Wiley and Sons
Year: 2005
Tongue: English
Weight: 96 KB
Volume: 11
Category: Article
ISSN: 1527-6465
DOI: 10.1002/lt.20463

No coin nor oath required. For personal study only.

✦ Synopsis

Liver involvement in hereditary hemorrhagic telangiectasia may lead to high-output cardiac failure. Few data have been reported on orthotopic liver transplantation (OLT) for these patients. In this paper, we describe two patients treated by OLT as a salvage procedure for cardiac failure, and we review literature on this subject. Our two patients resumed normal cardiac function after OLT. This procedure appears to be a promising therapy with good long-term results despite dissection difficulties encountered due to the collateral arterial network reorganization.

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