✦ LIBER ✦

Leigh's disease with decreased activities of pyruvate carboxylase and pyruvate decarboxylase

✍ Scribed by J. P. G. M. Van Biervliet; M. Duran; S. K. Wadman; J. F. Koster; A. van Rossum

Publisher: Springer
Year: 1979
Tongue: English
Weight: 521 KB
Volume: 2
Category: Article
ISSN: 0141-8955
DOI: 10.1007/bf01805557

No coin nor oath required. For personal study only.

📜 SIMILAR VOLUMES

The pyruvate branch point in fish liver

The pyruvate branch point in fish liver mitochondria: Effects of acylcarnitine oxidation on pyruvate dehydrogenase and pyruvate carboxylase activities

✍ Raul K. Suarez; Peter W. Hochachka 📂 Article 📅 1981 🏛 Springer 🌐 English ⚖ 515 KB

Pyruvate carboxylase activity is not abn

Pyruvate carboxylase activity is not abnormal in fibroblasts of patients with Friedreich's ataxia

✍ U. J. Dijkstra; J. M. F. Trijbels; W. Ruitenbeek; J. A. J. M. Bakkeren; A. J. M. 📂 Article 📅 1984 🏛 John Wiley and Sons 🌐 English ⚖ 105 KB 👁 2 views

childhood despite reported cases, we are, to our knowledge, ## Activity of Pyruvute Carboxylase in Fibroblasts reporting the youngest affected patient. Central pontine myelinolysis is attributed to overly rapid correction of hyponatremia, as occurred in this patient, although the precise mechani

The interaction of granaticin with nucle

The interaction of granaticin with nucleic acids and pyruvate decarboxylase

✍ Gail Gibson-Clay; Stephen R. Byrn; Peter Heinstein 📂 Article 📅 1982 🏛 John Wiley and Sons 🌐 English ⚖ 278 KB

The interaction of granaticin with two different yeast ribonucleic acids, dialyzed transfer RNA and calf thymus DNA was studied. Contrary to previous reports, no binding of granaticin to DNA or RNA was observed. The visible spectrum of granaticin on direct mixing or equilibrium dialysis of granatici

Pyruvate dehydrogenase activity is not d

Pyruvate dehydrogenase activity is not deficient in the brain of three autopsied cases with Leigh disease (subacute necrotizing encephalomyelopathy, SNE)

✍ B. Kustermann-Kuhn; K. Harzer; R. Schröder; W. Permanetter; J. Peiffer 📂 Article 📅 1984 🏛 Springer 🌐 English ⚖ 319 KB

In autopsied brain tissue from three cases with Leigh disease (subacute necrotizing encephalomyelitis, SNE) and controls, the activity of pyruvate dehydrogenase complex (PDHC) was determined under different conditions. It was found to be at the control level or increased, but not deficient. The acti

Photosynthetic characteristics and effec

Photosynthetic characteristics and effect of ATP in transgenic rice with phosphoenolpyruvate carboxylase and pyruvate orthophosphate dikinase genes

✍ B. J. Zhang; L. L. Ling; R. F. Wang; D. M. Jiao 📂 Article 📅 2009 🏛 Springer Netherlands 🌐 English ⚖ 427 KB

Steady-state and transient-state analysi

Steady-state and transient-state analysis of growth and metabolite production in a Saccharomyces cerevisiae strain with reduced pyruvate-decarboxylase activity

✍ Marcel T. Flikweert; Marko Kuyper; Antonius J. A. van Maris; Peter Kötter; Johan 📂 Article 📅 1999 🏛 John Wiley and Sons 🌐 English ⚖ 165 KB 👁 2 views

Pyruvate decarboxylase is a key enzyme in the production of low-molecular-weight byproducts (ethanol, acetate) in biomass-directed applications of Saccharomyces cerevisiae. To investigate whether decreased expression levels of pyruvate decarboxylase can reduce byproduct formation, the PDC2 gene, whi