Intraabdominal desmoplastic small cell tumor: Report and discussion of five cases
β Scribed by Robert J. Amato; Julie A. Ellerhorst; Alberto G. Ayala
- Publisher
- John Wiley and Sons
- Year
- 1996
- Tongue
- English
- Weight
- 809 KB
- Volume
- 78
- Category
- Article
- ISSN
- 0008-543X
No coin nor oath required. For personal study only.
β¦ Synopsis
BACKGROUND.
Intraabdominal desmoplastic small cell tumor is a rare malignancy that has only recently been described. In the adult population, it is usually seen in young males. The tumor appears to arise as a dominant mass or masses in the abdominal cavity, particularly in the pelvic region, without a clear visceral origin. Multiple small tumor nodules may be found attached to the peritoneal surface. Visceral metastases occur late in the clinical course, ultimately leading to the patient's death. Five young adults with intraabdominal desmoplastic small cell tumors were treated with aggressive chemotherapy.
π SIMILAR VOLUMES
Desmoplastic small round cell tumor (DSRCT) is a rare neoplasm mainly affecting young males and typically located in the abdomen. Prognosis is generally very poor. We report a rare case of paratesticular DSRCT in a 17-year-old boy, presenting with an isolated left scrotal mass. The patient had an ex
## BACKGROUND. Desmoplastic small round-cell tumor has been identified as a neoplasm with multidirectional immunohistochemical differentiation. The combination of topographic, morphologic, immunohistochemical, and molecular features of this tumor sets it apart as a pathologic entity. The optimal t