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Infantile cortical hyperostosis associated with the Wiskott-Aldrich syndrome

✍ Scribed by M. Abinun; M. Mikuška; B. Filipović

Publisher
Springer
Year
1988
Tongue
English
Weight
539 KB
Volume
147
Category
Article
ISSN
0340-6997

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✦ Synopsis

A case report of an infant with the Wiskott-Aldrich syndrome and clinical and radiological features of infantile cortical hyperostosis (Caffey disease) is presented. This is the third case described of the association of these two rare disorders and gives further support to the role of an immunologic defect in the pathogenesis of infantile cortical hyperostosis.

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