## X-linked adrenoleukodystrophy (X-ALD) is a neurodegenerative disorder caused by an impairment in peroxisomal โค-oxidation of very long straight-chain fatty acids (VLCFAs). Six clinical phenotypes have been delineated: childhood cerebral (CCALD), adolescent cerebral (AdolCALD), adult cerebral (ACAL
Incidence of X-linked adrenoleukodystrophy and the relative frequency of its phenotypes
โ Scribed by Bezman, Lena; Moser, Hugo W.
- Publisher
- John Wiley and Sons
- Year
- 1998
- Tongue
- English
- Weight
- 28 KB
- Volume
- 76
- Category
- Article
- ISSN
- 0148-7299
- DOI
- 10.1002/(sici)1096-8628(19980413)76:5<415::aid-ajmg9>3.0.co;2-l
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