Improvement of severe trunk spasms by bilateral high-frequency stimulation of the motor thalamus in a patient with chorea-acanthocytosis
✍ Scribed by Pierre Burbaud; Alain Rougier; Xavier Ferrer; Dominique Guehl; E. Cuny; Pierre Arne; Ch. Gross; B. Bioulac
- Publisher
- John Wiley and Sons
- Year
- 2002
- Tongue
- English
- Weight
- 511 KB
- Volume
- 17
- Category
- Article
- ISSN
- 0885-3185
- DOI
- 10.1002/mds.1260
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✦ Synopsis
Abstract
We report on a patient with a severe form of chorea‐acanthocytosis, intractable to medical treatment, who benefited from bilateral high‐frequency stimulation (HFS) of the posterior ventral oral nucleus of the thalamus. The frequency of trunk spasms dramatically decreased after surgery and the clinical benefit remained stable 1 year later. However, no clear effect was observed on dysarthria nor on hypotonia, which always impaired gait. We propose that HFS of the motor thalamus is a potential treatment for choreic or truncal dystonic symptoms whenever hypotonia is not the main feature of the syndrome. © 2001 Movement Disorder Society