Immunochemical studies of cultured fibroblasts from a patient with 3-ketothiolase deficiency
β Scribed by S. Yamaguchi; T. Orii; N. Sakura; S. Miyazawa; T. Hashimoto
- Publisher
- Springer
- Year
- 1988
- Tongue
- English
- Weight
- 253 KB
- Volume
- 11
- Category
- Article
- ISSN
- 0141-8955
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A patient is described with typical skin lesions of lichen myxedematosus and IgG-type lambda paraproteinemia. Fibroblasts cultured from the skin of the patient and from the skin of control persons were used to study glycosaminoglycan and collagen synthesis; the cultures were labelled with SHglucosam