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Hand tremor and orofacial dyskinesia: Clinical manifestations of glutaric aciduria type I in a young girl

✍ Scribed by Emilio Fernández-Álvarez; Angeles García-Cazorla; Anna Sans; Cristina Boix; María Antonia Vilaseca; Christianne Busquets; Antonia Ribes


Publisher
John Wiley and Sons
Year
2003
Tongue
English
Weight
725 KB
Volume
18
Category
Article
ISSN
0885-3185

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✦ Synopsis


Abstract

A 16‐year‐old girl with a history of postural hand tremor was investigated. Magnetic resonance imaging, biochemical, enzymatic, and molecular studies demonstrated glutaric aciduria type I (GA1). Now, at 19 years of age, focal dystonia and oral dyskinesia are also present. This is the first reported case of GA1 with such clinical phenotype. © 2003 Movement Disorder Society