Regulation of mitochondrial fatty acid Ξ²
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Bastin, Jean
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Article
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2014
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Elsevier Science
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English
β 899 KB
The mitochondrial fatty acid Ξ²-oxidation (FAO) pathway plays a crucial role in ATP production in many tissues with high-energy demand. This is highlighted by the diverse and possibly severe clinical manifestations of inborn fatty acid Ξ²-oxidation deficiencies. More than fifteen genetic FAO enzyme de